TY - JOUR
T1 - Aggregation-resistant alpha-synuclein tetramers are reduced in the blood of Parkinson's patients
AU - de Boni, Laura
AU - Wallis, Amber
AU - Hays Watson, Aurelia
AU - Ruiz-Riquelme, Alejandro
AU - Leyland, Louise-Ann
AU - Bourinaris, Thomas
AU - Hannaway, Naomi
AU - Wüllner, Ullrich
AU - Peters, Oliver
AU - Priller, Josef
AU - Falkenburger, Björn H
AU - Wiltfang, Jens
AU - Bähr, Mathias
AU - Zerr, Inga
AU - Bürger, Katharina
AU - Perneczky, Robert
AU - Teipel, Stefan
AU - Löhle, Matthias
AU - Hermann, Wiebke
AU - Schott, Björn-Hendrik
AU - Brockmann, Kathrin
AU - Spottke, Annika
AU - Haustein, Katrin
AU - Breuer, Peter
AU - Houlden, Henry
AU - Weil, Rimona S
AU - Bartels, Tim
N1 - © 2024. The Author(s).
PY - 2024/6/5
Y1 - 2024/6/5
N2 - Synucleinopathies such as Parkinson's disease (PD) are defined by the accumulation and aggregation of the α-synuclein protein in neurons, glia and other tissues. We have previously shown that destabilization of α-synuclein tetramers is associated with familial PD due to SNCA mutations and demonstrated brain-region specific alterations of α-synuclein multimers in sporadic PD patients following the classical Braak spreading theory. In this study, we assessed relative levels of disordered and higher-ordered multimeric forms of cytosolic α-synuclein in blood from familial PD with G51D mutations and sporadic PD patients. We used an adapted in vitro-cross-linking protocol for human EDTA-whole blood. The relative levels of higher-ordered α-synuclein tetramers were diminished in blood from familial PD and sporadic PD patients compared to controls. Interestingly, the relative amount of α-synuclein tetramers was already decreased in asymptomatic G51D carriers, supporting the hypothesis that α-synuclein multimer destabilization precedes the development of clinical PD. Our data, therefore suggest that measuring α-synuclein tetramers in blood may have potential as a facile biomarker assay for early detection and quantitative tracking of PD progression.
AB - Synucleinopathies such as Parkinson's disease (PD) are defined by the accumulation and aggregation of the α-synuclein protein in neurons, glia and other tissues. We have previously shown that destabilization of α-synuclein tetramers is associated with familial PD due to SNCA mutations and demonstrated brain-region specific alterations of α-synuclein multimers in sporadic PD patients following the classical Braak spreading theory. In this study, we assessed relative levels of disordered and higher-ordered multimeric forms of cytosolic α-synuclein in blood from familial PD with G51D mutations and sporadic PD patients. We used an adapted in vitro-cross-linking protocol for human EDTA-whole blood. The relative levels of higher-ordered α-synuclein tetramers were diminished in blood from familial PD and sporadic PD patients compared to controls. Interestingly, the relative amount of α-synuclein tetramers was already decreased in asymptomatic G51D carriers, supporting the hypothesis that α-synuclein multimer destabilization precedes the development of clinical PD. Our data, therefore suggest that measuring α-synuclein tetramers in blood may have potential as a facile biomarker assay for early detection and quantitative tracking of PD progression.
UR - https://www.scopus.com/pages/publications/85195313330
U2 - 10.1038/s44321-024-00083-5
DO - 10.1038/s44321-024-00083-5
M3 - Article
C2 - 38839930
SN - 1757-4676
JO - EMBO Molecular Medicine
JF - EMBO Molecular Medicine
ER -