Granulomatosis with polyangiitis and constrictive pericarditis--a case report

A E Horne, P A Henriksen, E N Amft

Research output: Contribution to journalArticlepeer-review

Abstract

Polyangiitis with granulomatosis, previously known as Wegener's granulomatosis, is a systemic necrotising granulomatous vasculitis. It predominantly affects the upper and lower respiratory tracts and the kidneys, but can potentially affect any organ system. It is diagnosed by clinical features, immunology (anti-neutrophil cytoplasmic antibodies) and histology. Cardiac involvement occurs in 6 to 44% of cases. We present a case of polyangiitis with granulomatosis and constrictive pericarditis, which occurred despite vigorous immunosuppression and which required surgical pericardectomy.

Original languageEnglish
Pages (from-to)283-5
Number of pages3
JournalJournal of the Royal College of Physicians of Edinburgh
Volume44
Issue number4
DOIs
Publication statusPublished - 2014

Keywords / Materials (for Non-textual outputs)

  • Adult
  • Colchicine/therapeutic use
  • Dyspnea/etiology
  • Echocardiography, Doppler
  • Female
  • Granulomatosis with Polyangiitis/complications
  • Humans
  • Pericarditis, Constrictive/diagnosis

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