Variably protease-sensitive prionopathy, a unique prion variant with inefficient transmission properties

Abigail B. Diack, Diane L. Ritchie, Alexander H. Peden, Deborah Brown, Aileen Boyle, Laura Morabito, David Maclennan, Paul Burgoyne, Casper Jansen, Richard S. Knight, Pedro Piccardo, James W. Ironside, Jean C. Manson^*